Dafallah Mumen Abdalazim, Habour Elsanosi, Ragab Esraa Ahmed, Shouk Zahraa Mamoun, Izzadden Mohammed
Faculty of Medicine, University of Gezira, Gezira, Sudan.
Wad Medani Pediatric Teaching Hospital, Wad Medani, Sudan.
Egypt J Neurol Psychiatr Neurosurg. 2021;57(1):85. doi: 10.1186/s41983-021-00339-8. Epub 2021 Jun 29.
Idiopathic intracranial hypertension is a rare neurological disorder of unknown etiology. It is characterized by symptoms and signs of raise intra cranial pressure, normal brain neuroimaging, and high opening pressure ≥ 280 cm H2O in the presence of normal cerebro spinal fluid constituents.
Ten years old thin boy presented with severe throbbing headache, vomiting, and visual obscurations for a duration of 10 days. Physical examination revealed body mass index of 14.8, VI and VII cranial nerve palsies. Fudoscopy showed grade 4 papilledema; brain CT and MRI were normal. Lumbar puncture revealed pressure of 300 cm H2O with normal CSF constituents. He was treated with acetazolamide, methylprednisolone, and paracetamol.
Pediatricians need to be more aware of idiopathic intracranial hypertension as it can lead to permanent vision loss.
特发性颅内高压是一种病因不明的罕见神经系统疾病。其特征为颅内压升高的症状和体征、脑部神经影像学检查正常，以及在脑脊液成分正常的情况下，初压≥280 cm H₂O。
一名10岁瘦弱男孩出现严重搏动性头痛、呕吐和视力模糊10天。体格检查显示体重指数为14.8，第VI和第VII颅神经麻痹。眼底镜检查显示4级视乳头水肿；脑部CT和MRI正常。腰椎穿刺显示压力为300 cm H₂O，脑脊液成分正常。他接受了乙酰唑胺、甲泼尼龙和对乙酰氨基酚治疗。
儿科医生需要更加了解特发性颅内高压，因为它可能导致永久性视力丧失。
