Schuster Blanca, Mayr Johannes
Department of Pediatric Surgery, University Children's Hospital Basel, Basel, Switzerland.
BMJ Case Rep. 2017 Jun 19;2017:bcr-2017-219310. doi: 10.1136/bcr-2017-219310.
Acute pneumatosis cystoides intestinalis (PCI) has been described after bone marrow transplantation (BMT). Several case series have demonstrated successful conservative treatment of PCI in children. We present a child with Fanconi anaemia, who developed severe graft versus host disease of the gastrointestinal tract, skin and liver after BMT and an acute, severe form of PCI. Our case report illustrates the complexity of diagnostic and therapeutic procedures in PCI in immunocompromised children.
急性肠壁囊样积气症(PCI)在骨髓移植(BMT)后已有报道。多个病例系列表明儿童PCI采用保守治疗可取得成功。我们报告一名患有范可尼贫血的儿童,其在BMT后出现了严重的胃肠道、皮肤和肝脏移植物抗宿主病以及急性重症PCI。我们的病例报告说明了免疫功能低下儿童PCI诊断和治疗程序的复杂性。