Avdeev S N
Research Institute of Pulmonology, Federal Biomedical Agency of Russia, Moscow, Russia.
Ter Arkh. 2017;89(1):112-122. doi: 10.17116/terarkh2017891112-122.
Idiopathic pulmonary fibrosis ((IPF) is the most common disease from a group of interstitial lung diseases, which occurs mainly in middle-aged and elderly people. Over the past decade, there have been considerable changes in approaches to diagnosing and treating IPF. The paper presents an update on the epidemiology of IPF, the results of new studies of its pathogenesis, and main approaches to diagnosing the disease. In addition, there is new evidence on therapy for IPF.
特发性肺纤维化(IPF)是间质性肺疾病中最常见的一种,主要发生在中老年人中。在过去十年中,IPF的诊断和治疗方法发生了显著变化。本文介绍了IPF的流行病学最新情况、其发病机制的新研究结果以及该疾病的主要诊断方法。此外,还有关于IPF治疗的新证据。