Terao Tohru, Kato Naoki, Ishii Takuya, Hatano Keisuke, Takeishi Hideaki, Kakizaki Shota, Tani Satoshi, Murayama Yuichi
Department of Neurosurgery, Atsugi City Hospital, Atsugi, Japan.
Department of Neurosurgery, The Jikei University School of Medicine, Tokyo, Japan.
NMC Case Rep J. 2016 May 16;3(3):91-95. doi: 10.2176/nmccrj.cr.2015-0295. eCollection 2016 Jul.
We present a rare case of spontaneous hemorrhage of a spinal ependymoma in the filum terminale presenting with acute cauda equina syndrome. A 16-year-old male presented with a sudden onset of severe back pain that began 10 days before hospitalization. This symptom progressed, followed by development of decreased sensation in the lower extremities, bladder dysfunction, and motor weakness that advanced to an inability to walk. Spinal magnetic resonance imaging revealed a hemorrhagic mass from Th12 to L2 and L4 to L5, and clinical signs indicated acute cauda equina compression. One day after admission to the hospital, emergency surgery was performed. A spinal tumor in the conus portion with a spinal subarachnoid hemorrhage was seen. Gross total excision of the massive hematoma mixed with the underlying tumor was performed. Pathological findings of the excised tumor demonstrated a WHO Grade II cellular ependymoma of the non-myxopapillary type. The patient made a significant recovery. The ability to walk was restored, and impaired bladder function improved at follow-up. Early diagnosis and suitable treatment are associated with a more favorable outcome.
我们报告一例罕见的终丝脊髓室管膜瘤自发性出血病例,该患者表现为急性马尾综合征。一名16岁男性在住院前10天突然出现严重背痛。此症状逐渐加重,随后出现下肢感觉减退、膀胱功能障碍及运动无力,进而发展至无法行走。脊髓磁共振成像显示胸12至腰2及腰4至腰5处有一出血性肿块,临床体征提示急性马尾神经受压。入院一天后进行了急诊手术。术中可见圆锥部有一脊髓肿瘤伴脊髓蛛网膜下腔出血。对与潜在肿瘤混合的巨大血肿进行了全切除。切除肿瘤的病理结果显示为世界卫生组织II级非黏液乳头型细胞性室管膜瘤。患者恢复良好。随访时步行能力恢复,膀胱功能障碍改善。早期诊断和适当治疗与更有利的预后相关。