Kutty Raja K, Ohmori Kazumi, Yamada Yasuhiro, Kato Yoko
Department of Neurosurgery, Government Medical College, Trivandrum, Kerala, India.
Department of Neurosurgery, Nishinomiya Watanabe Cardiovascular Center, Nishinomiya City, Hyuogo, Japan.
Asian J Neurosurg. 2020 Feb 25;15(1):190-193. doi: 10.4103/ajns.AJNS_233_19. eCollection 2020 Jan-Mar.
Ependymoma is a rare tumor central nervous system that arises from the ependymal lining of the ventricles or the central canal of the spinal cord. They are of neuroectodermal in origin and constitute about 30%-86% of tumors arising in the spinal cord. The occurrence of these tumors in the cervicomedullary region is very rare. Sudden symptomatic neurologic presentations due to hemorrhage in cervicomedullary ependymoma is very rare and so far have never been reported. Mostly presenting as neurologic deficits involving limbs, these tumors pose a technical challenge in their removal. We present a patient who presented with sudden-onset dysesthesia of the upper and lower limbs. On imaging, he was found to have a cystic medullary tumor extending to the cervical region with hemorrhage. We discuss the epidemiology, surgical challenges, and outcome along with review of literature of these rare tumors located in this precarious location.
室管膜瘤是一种罕见的中枢神经系统肿瘤,起源于脑室或脊髓中央管的室管膜内衬。它们起源于神经外胚层,约占脊髓肿瘤的30%-86%。这些肿瘤发生在颈髓区域非常罕见。颈髓室管膜瘤出血导致的突发症状性神经表现非常罕见,迄今为止从未有过报道。这些肿瘤大多表现为涉及肢体的神经功能缺损,在切除时面临技术挑战。我们报告一名患者,其出现上下肢突发感觉异常。影像学检查发现他有一个延伸至颈部区域并伴有出血的囊性髓内肿瘤。我们结合对位于这个危险部位的这些罕见肿瘤的文献回顾,讨论其流行病学、手术挑战及治疗结果。