Deparment of Pediatrics, Indiana University School of Medicine, Indianapolis, IN, USA.
Department of Pediatric Cardiology, Indiana University School of Medicine, Indianapolis, IN, USA.
World J Pediatr Congenit Heart Surg. 2020 Jul;11(4):NP31-NP33. doi: 10.1177/2150135117692979. Epub 2017 Jul 4.
Aortic regurgitation (AR) is a life-threatening complication of Takayasu arteritis (TA). Takayasu arteritis is a large-vessel vasculitis with a predominance in young adolescent and adult females. Inflammation involves the aorta and its major branches resulting in arterial dilatation, stenosis, aneurysm, occlusion, and thrombosis formation. Pediatric TA cases have been reported to also cause severe complications such as coronary aneurysms, retinopathy, and hypertension due to renovascular stenosis. In this report, we present a rare occurrence of infantile TA with severe AR requiring surgical intervention after failing medical therapy. Due to the patient's age and clinical status, a valve-sparing aortic annuloplasty with aortoplasty was performed.
主动脉瓣反流(AR)是 Takayasu 动脉炎(TA)的一种危及生命的并发症。Takayasu 动脉炎是一种大血管炎,主要发生在青少年和成年女性中。炎症累及主动脉及其主要分支,导致动脉扩张、狭窄、动脉瘤、闭塞和血栓形成。据报道,儿科 TA 病例也会因肾血管狭窄导致严重并发症,如冠状动脉瘤、视网膜病变和高血压。在本报告中,我们介绍了一例罕见的婴儿 TA 病例,该病例因严重的 AR 而需要在药物治疗失败后进行手术干预。由于患者年龄和临床状况,进行了保留瓣膜的主动脉瓣环成形术和主动脉成形术。