Campora Michela, Olivero Alberto, Toncini Carlo, Spina Bruno, Fulcheri Ezio, Terrone Carlo, Vellone Valerio Gaetano
Anatomic Pathology, Department of Integrated Surgical and Diagnostic Sciences, University of Genoa, Genoa, Italy.
Urology, Department of Integrated Surgical and Diagnostic Sciences, University of Genoa, Genoa, Italy.
Urology. 2017 Oct;108:e3-e5. doi: 10.1016/j.urology.2017.06.013. Epub 2017 Jul 3.
We investigate a patient with right kidney agenesis. Imaging showed the presence of a cystic mass dislocating the bladder. The specimen showed three formations: a kidney remnant, a ureter with blind-ending branch, and a cyst, from which departed another tubular structure, considered the deferential duct. The specimen was sampled. The supposed kidney was formed by cystic structures. Examination of the tubular structures disclosed smooth muscle fibers with no lumen, whereas the cyst was surrounded by fibrous and hemorrhagic walls. Collaboration among specialists allowed the diagnosis of Zinner syndrome, a congenital malformation due to an abnormal development of the Wolffian duct.
我们对一名右肾缺如的患者进行了研究。影像学检查显示有一个囊性肿物使膀胱移位。标本显示有三种结构：一个肾残余、一条有盲端分支的输尿管以及一个囊肿，从该囊肿发出另一个管状结构，考虑为输精管。对标本进行了取样。推测的肾脏由囊性结构构成。对管状结构的检查发现有平滑肌纤维但无管腔，而囊肿被纤维性和出血性壁所包围。专家之间的协作得出了Zinner综合征的诊断，这是一种由于中肾管发育异常导致的先天性畸形。
