Zinner 综合征的多种罕见临床变异型。
A wide spectrum of rare clinical variants of Zinner syndrome.
机构信息
Urology, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India.
Urology, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India
出版信息
BMJ Case Rep. 2021 Jan 18;14(1):e239254. doi: 10.1136/bcr-2020-239254.
Congenital malformations of the seminal vesicles (SVs) are rare and are associated with abnormalities of the ipsilateral urinary tracts as embryologically both the ureteral buds and SVs arise from the mesonephric ducts. The triad of SV cysts, ipsilateral renal agenesis and ejaculatory duct obstruction is known as the Zinner syndrome. We, herein, present three very rare presentations of Zinner syndrome. Case 1 presented with haematuria, and was found to have a large SV cyst with stones and underwent a robotic cyst excision. Case 2 presented with primary infertility, and was found to have a variant of Zinner syndrome. Case 3 was a known case of chronic kidney disease on maintenance haemodialysis who presented with fever and oliguria. He was found to have Zinner syndrome and underwent aspiration of SV abscess. To the best of our knowledge, such varying presentations of Zinner syndrome have been rarely reported thus far.
先天性精囊畸形（SVs）较为罕见，与同侧尿路异常有关，因为输尿管芽和 SVs 均起源于中肾管。SV 囊肿、同侧肾发育不全和射精管梗阻三联征称为 Zinner 综合征。本文报告了 3 例非常罕见的 Zinner 综合征。病例 1 以血尿就诊，发现有一个大的 SV 囊肿伴结石，行机器人囊肿切除术。病例 2 以原发性不育就诊，发现存在 Zinner 综合征的变异型。病例 3 为慢性肾脏病行维持性血液透析的已知病例，以发热和少尿就诊。发现存在 Zinner 综合征，行 SV 脓肿抽吸术。据我们所知，迄今很少有关于 Zinner 综合征如此不同表现的报道。
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