Kagalwalla Mustafa, Gupta Medhavi, Malwi Umme Haani, Hussain Nazia
Internal Medicine, Mount Sinai Saint Luke's Hospital Center.
Medical Student, Gandhi Medical College, Bhopal, MP.
Cureus. 2017 Jun 1;9(6):e1303. doi: 10.7759/cureus.1303.
Systemic sclerosis is a connective tissue disorder that frequently involves the heart. All cardiac structures can be involved but aortic valve involvement is rare. We report a case of an 83-year-old man with a history of systemic sclerosis presenting with shortness of breath. A transthoracic echocardiogram revealed severe aortic stenosis that could not be explained by other causes. These patients often pose challenges in management as they are not surgical candidates. Transaortic valvular implantation is a viable option for these patients.
系统性硬化症是一种常累及心脏的结缔组织疾病。所有心脏结构均可受累,但主动脉瓣受累罕见。我们报告一例83岁有系统性硬化症病史的男性,出现呼吸急促症状。经胸超声心动图显示严重主动脉瓣狭窄,无法用其他原因解释。这些患者在管理上常常带来挑战,因为他们不适合手术。经主动脉瓣膜植入对这些患者是一种可行的选择。