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一名22岁患者以咯血为表现的原发性心脏平滑肌肉瘤:一种罕见疾病的不寻常表现

Primary cardiac leiomyosarcoma presenting as haemoptysis in a 22-year-old patient: an unusual presentation of a rare condition.

作者信息

Hassan Masroor, Khattak Maria, Abdullah Hafez Mohammad Ammar, Nasib Bushra

机构信息

Department of Histo-Pathology, Rehman Medical Institute, Peshawar, Pakistan.

Department of Internal Medicine, Khyber Teaching Hospital, Peshawar, Pakistan.

出版信息

BMJ Case Rep. 2017 Jul 13;2017:bcr-2017-219416. doi: 10.1136/bcr-2017-219416.

Abstract

Primary cardiac sarcomas are rare malignant tumours and among them, leiomyosarcoma is extremely rare. They are especially rare in a young age group. We present a case of a 22-year-old male patient with primary leiomyosarcoma of the left atrium involving the pulmonary veins who presented with haemoptysis and shortness of breath. He underwent surgical excision of the tumour along with mitral valve replacement followed by adjuvant chemotherapy. No recurrence was reported on his second 6 monthly follow-ups.

摘要

原发性心脏肉瘤是罕见的恶性肿瘤,其中平滑肌肉瘤极为罕见。在年轻人群中尤其罕见。我们报告一例22岁男性患者,患有累及肺静脉的左心房原发性平滑肌肉瘤,表现为咯血和气短。他接受了肿瘤手术切除及二尖瓣置换术,随后进行辅助化疗。在第二次每6个月的随访中未报告复发情况。

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Eur J Cardiothorac Surg. 2013 Aug;44(2):330-5; discussion 335-6. doi: 10.1093/ejcts/ezt029. Epub 2013 Feb 7.
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