Belsha Dalia, Narula Priya, Urs Arun, Thomson Mike
Dalia Belsha, Priya Narula, Arun Urs, Mike Thomson, Centre of Paediatric Gastroenterology, Sheffield Children's Hospital, Sheffield S10 2TH, United Kingdom.
World J Gastrointest Endosc. 2017 Jul 16;9(7):341-345. doi: 10.4253/wjge.v9.i7.341.
We report a case of an infant with Menkes' disease (MD) presented at the age of five months, with coffee ground vomiting, melaena with a significant drop of haemoglobin. Urgent endoscopic assessment revealed a friable bleeding trans-pyloric multi-lobulated sessile polyp. Due to further significant upper gastrointestinal bleeding, polypectomy occurred. Endoscopic mucosal resection was performed with a grasp-and-snare technique using a dual channel operating gastroscope. Haemostasis was achieved by application of argon plasma coagulation where required. No perforation occurred. Repeated debridement was required 6 wk after which the growth was excised completely with no further blood transfusion required after that procedure. Histological examination confirmed ulcerated and inflamed hyperplastic polyp. We discuss our endoscopic technique and discuss the reported gastrointestinal manifestation of MD in the literature.
我们报告一例5个月大的患有门克斯病(MD)的婴儿病例,该婴儿出现咖啡渣样呕吐、黑便且血红蛋白显著下降。紧急内镜检查发现一个易碎的经幽门的多叶无蒂息肉伴出血。由于进一步出现严重的上消化道出血,遂进行了息肉切除术。使用双通道手术胃镜通过抓持圈套技术进行内镜黏膜切除术。必要时应用氩离子凝固术实现止血。未发生穿孔。6周后需要重复清创,之后完全切除增生组织,该手术后无需进一步输血。组织学检查证实为溃疡且发炎的增生性息肉。我们讨论了我们的内镜技术,并讨论了文献中报道的MD的胃肠道表现。