Arasanz Esteban H, Hernández Marín B, Pérez Ricarte S, Lacalle Emborujo A, Pérez Ricarte L, Martínez Aguillo M
Complejo Hospitalario de Navarra.
An Sist Sanit Navar. 2017 Aug 31;40(2):309-314. doi: 10.23938/ASSN.0035.
Pulmonary epithelioid hemangioendothelioma is an uncommon neoplastic disease of endothelial origin, with an incidence inferior to one in a million. It usually behaves as a low-grade malignancy; nevertheless, a few cases have been described in which this tumour manifests a highly aggressive behavior, spreading throughout the organism. We report the case of a 77-year-old woman who was diagnosed with metastatic pulmonary epithelioid hemangioendothelioma with severe symptoms, requiring urgent treatment to palliate them. Key words. Epithelioid hemangioendothelioma. Lung.
肺上皮样血管内皮瘤是一种罕见的起源于内皮的肿瘤性疾病,发病率低于百万分之一。它通常表现为低度恶性;然而,已有少数病例报道显示该肿瘤具有高度侵袭性,可扩散至全身。我们报告一例77岁女性患者,被诊断为转移性肺上皮样血管内皮瘤,伴有严重症状,需要紧急治疗以缓解症状。关键词:上皮样血管内皮瘤。肺。