新生儿早期发绀的罕见原因：右肺动脉缺如。
A rare cause of early neonatal cyanosis: absent right pulmonary artery.
作者信息
Joshi Avadhesh, Kumar Manish, Arun Sumitha, Sheshrao Mane Manisha
机构信息
Department of Neonatology, Christian Medical College, Vellore, Tamil Nadu, India.
Department of Neonatology, Christian Medical College, Vellore, Tamilnadu, India.
出版信息
BMJ Case Rep. 2017 Aug 9;2017:bcr-2017-220978. doi: 10.1136/bcr-2017-220978.
Abstract
Unilateral absent right pulmonary artery is a rare developmental anomaly that usually presents in late childhood and adolescence as recurrent respiratory tract infections, dyspnoea and haemoptysis. We report a case of a 2-day-old baby with respiratory distress and differential cyanosis. Echocardiogram showed pulmonary hypertension with absent right pulmonary artery. The findings were confirmed by CT angiogram. The baby improved with pulmonary vasodilators and antifailure medications.
摘要
单侧右肺动脉缺如是一种罕见的发育异常，通常在儿童晚期和青少年期表现为反复呼吸道感染、呼吸困难和咯血。我们报告一例2日龄患有呼吸窘迫和差异性发绀的婴儿。超声心动图显示肺动脉高压伴右肺动脉缺如。CT血管造影证实了这些发现。该婴儿使用肺血管扩张剂和抗心力衰竭药物后病情好转。
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