• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

罗斯综合征中心脏和肌肉交感神经活动未受累:一项随访研究。

Absent cardiac and muscle sympathetic nerve activities involvement in Ross syndrome: A follow-up study.

作者信息

Fileccia E, Liguori R, Cortelli P, Donadio V

机构信息

Department of Biomedical and Neuromotor Sciences, University of Bologna, Italy.

Department of Biomedical and Neuromotor Sciences, University of Bologna, Italy; Institute of Neurological Sciences of Bologna-IRCCS, Bellaria Hospital, Bologna, Italy.

出版信息

Auton Neurosci. 2017 Dec;208:161-164. doi: 10.1016/j.autneu.2017.08.003. Epub 2017 Aug 9.

DOI:10.1016/j.autneu.2017.08.003
PMID:28807531
Abstract

PURPOSE

Ross syndrome (RS) is characterized by selective involvement of post-ganglionic skin sympathetic nerve fibres. We report a follow-up study in 4 patients to clarify whether in RS autonomic dysfunction spreads affecting also cardiovascular system.

METHODS

The patients underwent cardiovascular reflexes (CVR) and microneurography recording of muscle sympathetic nerve activity (MSNA) for a follow-up mean period of 5years.

RESULTS

CVR and MSNA were normal at baseline and unchanged over the follow-up.

CONCLUSIONS

Cardiovascular autonomic system is spared in RS differently from skin autonomic activity dysfunction which progress over time. However, before drawing any definite conclusion, a large cohort of patients needs to be studied.

摘要

目的

罗斯综合征(RS)的特征是节后皮肤交感神经纤维选择性受累。我们报告了对4例患者的随访研究,以阐明在RS中自主神经功能障碍是否会扩散并累及心血管系统。

方法

患者接受了心血管反射(CVR)和肌肉交感神经活动(MSNA)的微神经ography记录,随访平均时间为5年。

结果

CVR和MSNA在基线时正常,随访期间无变化。

结论

与随时间进展的皮肤自主神经活动功能障碍不同,RS患者的心血管自主神经系统未受累。然而,在得出任何明确结论之前,需要对大量患者进行研究。

相似文献

1
Absent cardiac and muscle sympathetic nerve activities involvement in Ross syndrome: A follow-up study.罗斯综合征中心脏和肌肉交感神经活动未受累:一项随访研究。
Auton Neurosci. 2017 Dec;208:161-164. doi: 10.1016/j.autneu.2017.08.003. Epub 2017 Aug 9.
2
Muscle and skin sympathetic activities in Ross syndrome.罗丝综合征的肌肉和皮肤交感活动。
Clin Neurophysiol. 2012 Aug;123(8):1639-43. doi: 10.1016/j.clinph.2011.11.263. Epub 2012 Jan 11.
3
Selective autonomic failure: Ross syndrome.选择性自主神经功能衰竭:罗斯综合征。
Clin Neurophysiol. 2012 Aug;123(8):1479-80. doi: 10.1016/j.clinph.2011.12.016. Epub 2012 Jan 20.
4
Cardiac sympathetic denervation in Ross syndrome demonstrated by MIBG-SPECT.
J Auton Nerv Syst. 1999 May 28;76(2-3):184-7. doi: 10.1016/s0165-1838(99)00018-1.
5
Teaching Video NeuroImages: Disorder of sweat, tonic pupil, and areflexia: Ross syndrome.教学视频神经影像:出汗障碍、强直性瞳孔和无反射:罗斯综合征。
Neurology. 2020 Sep 1;95(9):e1292-e1293. doi: 10.1212/WNL.0000000000010101. Epub 2020 Jun 30.
6
Tonic pupil, areflexia, and segmental anhidrosis: two additional cases of Ross syndrome and review of the literature.强直性瞳孔、无反射及节段性无汗症:另外两例罗斯综合征病例及文献综述
J Neurol. 1992 Apr;239(4):231-4. doi: 10.1007/BF00839146.
7
Polyneuropathy in Sjögren's syndrome. A case of prevalently autonomic neuropathy with tonic pupil and hypohidrosis.干燥综合征中的多发性神经病。一例以强直性瞳孔和少汗为主的自主神经病变病例。
Funct Neurol. 1988 Jul-Sep;3(3):337-48.
8
Microneurographic evaluation of sympathetic activity in small fiber neuropathy.小纤维神经病交感神经活性的微神经电图评估。
Clin Neurophysiol. 2011 Sep;122(9):1854-9. doi: 10.1016/j.clinph.2011.02.024. Epub 2011 Mar 23.
9
Isolated generalised anhidrosis induced by postganglionic sympathetic skin nerve fibre degeneration: an incomplete Ross syndrome?节后交感皮肤神经纤维变性引起的孤立性全身性无汗症:一种不完全性罗斯综合征?
J Neurol Neurosurg Psychiatry. 2008 Aug;79(8):959-61. doi: 10.1136/jnnp.2007.142802. Epub 2008 Mar 20.
10
Segmental facial anhidrosis and tonic pupils with preserved deep tendon reflexes: a novel autonomic neuropathy.节段性面部无汗、强直性瞳孔且深腱反射保留:一种新型自主神经病变。
J Neuroophthalmol. 2005 Mar;25(1):5-8. doi: 10.1097/00041327-200503000-00002.

引用本文的文献

1
Complete heart block in Ross syndrome.罗斯综合征中的完全性心脏传导阻滞。
HeartRhythm Case Rep. 2023 Aug 25;9(11):815-817. doi: 10.1016/j.hrcr.2023.08.012. eCollection 2023 Nov.
2
Clinical presentation and autonomic profile in Ross syndrome.罗斯综合征的临床表现及自主神经特征
J Neurol. 2021 Oct;268(10):3852-3860. doi: 10.1007/s00415-021-10531-8. Epub 2021 Apr 3.
3
Clinical and laboratory correlates of selective autonomic dysfunction due to Ross syndrome.罗斯综合征所致选择性自主神经功能障碍的临床及实验室相关因素
J Family Med Prim Care. 2019 Apr;8(4):1500-1503. doi: 10.4103/jfmpc.jfmpc_151_19.