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四叶式主动脉瓣合并主动脉瓣反流、二尖瓣反流及主动脉扩张

Quadricuspid Aortic Valve Associated with Aortic Regurgitation, Mitral Regurgitation, and Aortic Dilatation.

作者信息

Sivri Serkan, Bastug Serdal, Can Guney Murat, Alsancak Yakup, Ozdemir Elcin, Bozkurt Engin

机构信息

Ahi Evran University Education and Research Hospital, Division of Cardiology, Kırşehir, Turkey. Electronic correspondence:

Atatürk Education and Research Hospital, Division of Cardiology, Ankara, Turkey.

出版信息

J Heart Valve Dis. 2017 Mar;26(2):243-246.

PMID:28820561
Abstract

The quadricuspid aortic valve (QAV) is a very uncommon congenital malformation with an estimated incidence of 0.003% to 0.043% of all congenital heart diseases. Combinations of QAV with several different congenital malformations have been described. The case is reported of a type A QAV associated with moderate aortic regurgitation, mild mitral regurgitation, and ascending aorta dilatation. This interesting case was referred for close follow up.

摘要

四叶式主动脉瓣(QAV)是一种非常罕见的先天性畸形,在所有先天性心脏病中估计发病率为0.003%至0.043%。已有QAV与几种不同先天性畸形合并存在的报道。本文报告了1例A型QAV合并中度主动脉瓣反流、轻度二尖瓣反流及升主动脉扩张的病例。该有趣病例被转诊以进行密切随访。

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Quadricuspid Aortic Valve Associated with Aortic Regurgitation, Mitral Regurgitation, and Aortic Dilatation.四叶式主动脉瓣合并主动脉瓣反流、二尖瓣反流及主动脉扩张
J Heart Valve Dis. 2017 Mar;26(2):243-246.
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A quadricuspid aortic valve causing moderate aortic regurgitation.四叶式主动脉瓣导致中度主动脉瓣反流。
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