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孤立性先天性“C”型四叶式主动脉瓣:主动脉瓣关闭不全的罕见病因。

An Isolated Congenital Type 'C' Quadrileaflet Aortic Valve: A Rare Cause of Aortic Insufficiency.

作者信息

Kumar J Rajendra, Kumbhare Mamta B, Kumar P Goutham, Goud T Vishal

机构信息

Associate Professor.

Senior Specialist Anesthesia, Dhanvanthari Hospital, NTPC, RSTPS, Karimnagar, Andhra Pradesh.

出版信息

J Assoc Physicians India. 2016 Feb;64(2):80-81.

PMID:27730792
Abstract

An accessory coronary cusp in aortic valve is a rare congenital cardiovascular malformation with an estimated incidence of 0.003 to 0.043% of all congenital heart disease. It is also describe as a quadricuspid aortic valve (QAV). Several different anatomical variations of quadricuspid aortic valve have been described. Current technology enables noninvasive diagnosis in most cases. Here we reported a rare an isolated congenital type 'C' QAV with aortic regurgitation; hence it was worth reporting this interesting case.

摘要

主动脉瓣副冠状动脉瓣叶是一种罕见的先天性心血管畸形,在所有先天性心脏病中的发生率估计为0.003%至0.043%。它也被描述为四叶主动脉瓣(QAV)。已经描述了四叶主动脉瓣的几种不同解剖变异。目前的技术在大多数情况下能够进行无创诊断。在此,我们报告了一例罕见的孤立先天性C型QAV伴主动脉瓣反流病例;因此,报道这个有趣的病例很有价值。

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