An Isolated Congenital Type 'C' Quadrileaflet Aortic Valve: A Rare Cause of Aortic Insufficiency.

An accessory coronary cusp in aortic valve is a rare congenital cardiovascular malformation with an estimated incidence of 0.003 to 0.043% of all congenital heart disease. It is also describe as a quadricuspid aortic valve (QAV). Several different anatomical variations of quadricuspid aortic valve have been described. Current technology enables noninvasive diagnosis in most cases. Here we reported a rare an isolated congenital type 'C' QAV with aortic regurgitation; hence it was worth reporting this interesting case.