Khan Mohammad Harisullah, Kashif Ramsha, Rahim Khan Hamza Abdur, Fatimi Saulat Hasnain
Department of Cardiothoracic Surgery, Aga Khan University, Karachi, Pakistan.
J Ayub Med Coll Abbottabad. 2016 Oct-Dec;28(4):818-820.
Myxoid liposarcomas of the head and neck are mostly metastatic in nature, with the primary lesion usually in lower extremities or retroperitoneum. Primary mediastinal liposarcomas are even rarer. Although there have been previous cases reporting their incidence, there is no evidence of any case comprising of both the neck and the mediastinal region yet. We here present a case of a 43 year old male with a primary liposarcoma of the myxoid subtype originating in the anterior mediastinum. This is the first time such a case has presented in literature. The patient presented with a right sided neck swelling associated with pain and shortness of breath upon lying down. CT neck revealed an enhancing mass extending from right cervical region to axilla and encasing the subclavian artery and involving a portion of the right lung. The patient underwent wide local excision of the mass along with chemoradiotherapy to prevent recurrence.
头颈部黏液样脂肪肉瘤本质上大多是转移性的,原发灶通常位于下肢或腹膜后。原发性纵隔脂肪肉瘤更为罕见。尽管之前有病例报告过其发病率,但尚无证据表明有任何病例同时累及颈部和纵隔区域。我们在此报告一例43岁男性,患有起源于前纵隔的黏液样亚型原发性脂肪肉瘤。这是文献中首次报道此类病例。患者表现为右侧颈部肿胀,伴有疼痛,躺下时呼吸急促。颈部CT显示一个强化肿块,从右颈部区域延伸至腋窝,包绕锁骨下动脉并累及右肺的一部分。患者接受了肿块的广泛局部切除以及放化疗以预防复发。