原发性心脏平滑肌瘤导致右心室梗阻和三尖瓣反流。

Primary Cardiac Leiomyoma Causing Right Ventricular Obstruction and Tricuspid Regurgitation.

作者信息

Careddu Lucio, Foà Alberto, Leone Ornella, Agostini Valentina, Gargiulo Gaetano Domenico, Rapezzi Claudio, Di Bartolomeo Roberto, Pacini Davide

机构信息

Pediatric Cardiac Surgery, Department of Experimental, Diagnostic and Specialty Medicine, Alma Mater Studiorum-University of Bologna, S.Orsola-Malpighi University Hospital, Bologna, Italy.

Cardiology, Department of Experimental, Diagnostic and Specialty Medicine, Alma Mater Studiorum-University of Bologna, S.Orsola-Malpighi University Hospital, Bologna, Italy.

出版信息

Ann Thorac Surg. 2017 Sep;104(3):e231-e233. doi: 10.1016/j.athoracsur.2017.03.068.

DOI:10.1016/j.athoracsur.2017.03.068

PMID:28838514

Abstract

We report the unique case of a primary cardiac leiomyoma originating from the right ventricle and involving the tricuspid valve in a 43-year-old woman. Echocardiography showed a giant mass causing severe pulmonary stenosis and tricuspid valve regurgitation. The patient underwent surgical excision and histologic examination revealed a primary cardiac leiomyoma. To the best of our knowledge only three cases of primary cardiac leiomyoma have so far been reported, and this is the first case of primary cardiac leiomyoma involving the tricuspid valve apparatus.

摘要

我们报告了一例罕见病例，一名43岁女性患有起源于右心室并累及三尖瓣的原发性心脏平滑肌瘤。超声心动图显示一个巨大肿块，导致严重的肺动脉狭窄和三尖瓣反流。患者接受了手术切除，组织学检查显示为原发性心脏平滑肌瘤。据我们所知，迄今为止仅报道过三例原发性心脏平滑肌瘤病例，而这是首例累及三尖瓣装置的原发性心脏平滑肌瘤。