Bansal Smriti, Das Sima
Oculoplasty and Ocular Oncology Services, Dr. Shroff's Charity Eye Hospital, 5027 Kedar Nath Road, New Delhi 110002, India.
Saudi J Ophthalmol. 2017 Jul-Sep;31(3):196-198. doi: 10.1016/j.sjopt.2017.05.012. Epub 2017 May 25.
Cyclic oculomotor nerve paresis and spasm are a rare disorder characterized by alternating spastic and paretic phase of the muscles supplied by the oculomotor nerve. A 26-year-old male presented with abnormal right eyelid movements since early childhood. Examination findings were consistent with diagnosis of right eye cyclic oculomotor nerve palsy. A paretic phase with complete upper eyelid ptosis, exotropia, hypotropia and dilatation of the pupil was followed by a phase of orthotropia, the absence of ptosis and normal pupil size. The whole cycle was of about 100 s duration with patient having no voluntary control over the eyelid movements and ocular alignment. Systemic evaluation and neuroimaging were normal. A tarsofrontal silicone sling surgery done for the ptosis correction decreased the eyelid movements during different phases of the cycle.
周期性动眼神经麻痹和痉挛是一种罕见的疾病，其特征是动眼神经所支配肌肉的痉挛期和麻痹期交替出现。一名26岁男性自幼出现右眼睑运动异常。检查结果符合右眼周期性动眼神经麻痹的诊断。先是出现麻痹期，表现为上睑完全下垂、外斜视、下斜视和瞳孔散大，随后进入正位视期，此时上睑不下垂且瞳孔大小正常。整个周期持续约100秒，患者无法自主控制眼睑运动和眼球位置。全身评估和神经影像学检查均正常。为矫正上睑下垂而进行的睑额硅胶吊带手术减少了周期不同阶段的眼睑运动。
