Sorenson Karl R, Piovezani Ramos Guilherme, Villasboas Bisneto Jose Caetano, Price Katharine
Department of Internal Medicine, Mayo Clinic, Rochester, Minnesota, USA.
Department of Medicine, Division of Hematology, Mayo Clinic, Rochester, Minnesota, USA.
Case Rep Oncol. 2017 Aug 9;10(2):726-731. doi: 10.1159/000479499. eCollection 2017 May-Aug.
Salivary duct carcinoma is a rare malignancy associated with hormone receptor and human epidermal growth factor receptor 2 (HER2) overexpression. Local surgical control is the cornerstone of therapy, but a subset of patients develops metastatic disease portending a poor prognosis and limited management options. Intracranial metastases are an uncommon manifestation and present a therapeutic challenge. We report the case of a 31-year-old male who presented with facial pain and swelling subsequently diagnosed with salivary duct carcinoma. Our patient underwent extensive locoregional resection and analysis of the tumor tissue demonstrated evidence of androgen receptor expression and HER2 overexpression. His course was complicated by metastatic extra- and intracranial recurrence despite combined modality treatment with radiation and chemotherapy followed by anti-HER2 monoclonal antibody therapy and androgen deprivation therapy. After exhausting standard treatment options, he received experimental therapy with a new small-molecule tyrosine kinase inhibitor, neratinib, with evidence of a transient clinical response and no significant adverse effects. This case exemplifies the potential and limitations of targeted therapy, particularly when applied to patients with rare diseases and presentations.
涎腺导管癌是一种罕见的恶性肿瘤,与激素受体及人表皮生长因子受体2(HER2)过表达相关。局部手术控制是治疗的基石,但一部分患者会发生转移性疾病,预后较差且治疗选择有限。颅内转移是一种不常见的表现,带来了治疗挑战。我们报告一例31岁男性患者,其最初表现为面部疼痛和肿胀,随后被诊断为涎腺导管癌。我们的患者接受了广泛的局部区域切除术,肿瘤组织分析显示有雄激素受体表达及HER2过表达的证据。尽管接受了放疗、化疗联合抗HER2单克隆抗体治疗及雄激素剥夺治疗,其病程仍因颅外和颅内转移性复发而复杂化。在用尽标准治疗方案后,他接受了一种新型小分子酪氨酸激酶抑制剂奈拉替尼的试验性治疗,有短暂临床反应的证据且无明显不良反应。该病例例证了靶向治疗的潜力和局限性,尤其是应用于罕见疾病及表现的患者时。