一名无1型神经纤维瘤病患者手部掌骨原发性骨内恶性外周神经鞘瘤：1例罕见病例报告
Primary Intraosseous Malignant Peripheral Nerve Sheath Tumor of Metacarpal Bones of the Hand in a Patient Without Neurofibromatosis 1: Report of a Rare Case.
作者信息
Devnani Bharti, Biswas Ahitagni, Bakhshi Sameer, Khan Shah Alam, Mridha Asit Ranjan, Agarwal Shipra
机构信息
Department of Radiotherapy and Oncology, All Institute of Medical Sciences, New Delhi, India.
Department of Medical Oncology, All Institute of Medical Sciences, New Delhi, India.
出版信息
Indian J Med Paediatr Oncol. 2017 Apr-Jun;38(2):232-235. doi: 10.4103/ijmpo.ijmpo_5_17.
Malignant peripheral nerve sheath tumor (MPNST) usually arises in peripheral nerve sheath cells. The intraosseous location of MPNST is rare. Mandible is the most common site of bony involvement. Involvement of bones of the hand is quite unusual. We report a case of MPNST involving metacarpal bones of the left hand treated with surgery followed by adjuvant radiation and chemotherapy and review the pertinent literature.
恶性外周神经鞘膜瘤（MPNST）通常起源于外周神经鞘细胞。MPNST的骨内定位罕见。下颌骨是骨受累最常见的部位。手部骨骼受累相当不寻常。我们报告1例累及左手掌骨的MPNST病例，该病例接受了手术治疗，随后进行辅助放疗和化疗，并复习相关文献。
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