Sanz-Ruiz Pablo, Villanueva-Martinez Manuel, Calvo-Haro Jose Antonio, Carbó-Laso Esther, Vaquero-Martín Javier
Department of Traumatology and Orthopaedic Surgery, General University Hospital Gregorio Marañón, Madrid, Spain.
Arthroplast Today. 2017 Mar 6;3(3):154-159. doi: 10.1016/j.artd.2017.01.001. eCollection 2017 Sep.
Osteogenesis imperfecta (OI) is a rare congenital disease characterized by alterations in bone quality, with susceptibility to fractures, instability, deformities, and osteoarthrosis. Prosthetic surgery in these patients is associated with an abnormally high rate of implant failures. On the other hand, abnormal bone fragility adds to the complexity of revision surgery in such individuals-thus representing a genuine challenge for the orthopaedic surgeon. We present a case of femoral reconstruction in a patient with OI and prosthetic loosening after reconstruction secondary to femoral septic pseudoarthrosis. Intramedullary total femoral reconstruction was carried out after exceeding the biological reconstruction limits. This is the first reported instance of the use of an intramedullary total femur arthroplasty as salvage technique in an OI patient. This technique should be considered when we have exceeded biological limits for femoral fixation.
成骨不全症（OI）是一种罕见的先天性疾病，其特征是骨质改变，易发生骨折、不稳定、畸形和骨关节炎。这些患者的假体手术与异常高的植入失败率相关。另一方面，异常的骨脆性增加了此类个体翻修手术的复杂性，因此对骨科医生来说是一个真正的挑战。我们报告一例成骨不全症患者股骨重建的病例，该患者在股骨感染性假关节继发重建后出现假体松动。在超过生物学重建极限后进行了股骨髓内全重建。这是首次报道在成骨不全症患者中使用股骨髓内全髋关节置换术作为挽救技术的病例。当股骨固定超过生物学极限时，应考虑这种技术。
