Herath M, Siriwardena B S M S, Jayasinghe R D, Dias D K
Oral and Maxillofacial Surgery, Maxillofacial and Regional Cleft Centre, Teaching Hospital, Karapitiya, Galle, Sri Lanka.
Faculty of Dental Sciences, University of Peradeniya, Peradeniya, Sri Lanka.
Int J Oral Maxillofac Surg. 2018 Apr;47(4):442-444. doi: 10.1016/j.ijom.2017.08.011. Epub 2017 Sep 18.
Foetal oral teratoma or epignathus is a rare benign condition that originates in the oropharyngeal region. The term 'teratoma' refers to a mass composed of poorly organized tissues derived from each of the three germ layers. Epignathus may occur when one twin ceases development during gestation and becomes vestigial to the fully formed dominant twin. The reported incidence of epignathus is approximately 1:35,000 to 1:200,000 live births. A unique case of partial facial duplication with gross histological and radiological evidence of partial duplication of the facial elements and organs is presented herein. The affected newborn baby underwent urgent surgery due to breathing difficulties. The mass was excised successfully and the infant made an uneventful recovery. The resected specimen included two developing faces, each composed of a developing mandible and maxilla with developing tooth buds. Tissues from all three germ layers were present. In such cases, the treatment option is exclusively surgical, and complete resection is curative in most cases during the early neonatal period.
胎儿口腔畸胎瘤或附鼻畸胎是一种罕见的良性疾病，起源于口咽区域。“畸胎瘤”一词指的是由源自三个胚层的组织构成的结构不良的肿块。附鼻畸胎可能发生在一个双胞胎在妊娠期停止发育并成为发育完全的占主导地位的双胞胎的退化残留物时。据报道，附鼻畸胎的发病率约为每35,000至200,000例活产中有1例。本文介绍了一例独特的部分面部重复病例，有面部元素和器官部分重复的大体组织学和放射学证据。由于呼吸困难，受影响的新生儿接受了紧急手术。肿块被成功切除，婴儿顺利康复。切除的标本包括两张发育中的脸，每张脸都由一个发育中的下颌骨和上颌骨以及发育中的牙胚组成。三个胚层的组织都存在。在这种情况下，治疗选择完全是手术治疗，在新生儿早期，大多数情况下完全切除是可以治愈的。
