Division of Pediatric Cardiac Surgery, Department of Cardiothoracic Surgery, University Hospital Muenster, Muenster, Germany.
Department of Medicine A-Hematology, Oncology and Pneumology, University Hospital Muenster, Muenster, Germany.
World J Pediatr Congenit Heart Surg. 2020 Jul;11(4):NP69-NP71. doi: 10.1177/2150135117713740. Epub 2017 Sep 21.
Pulmonary artery sling (PAS) is a rare disease frequently associated with severe malacia and stenosis of the trachea. We present a two-day-old newborn that underwent urgent surgery for PAS and needed prolonged respiratory support afterward. Temporary airway stenting above the level of the tracheal bifurcation was performed five days after surgery to overcome severe airway obstruction caused by tracheomalacia and laceration of the tracheal mucosa after diagnostic bronchoscopy. Two days after the procedure, the child could be extubated and after two weeks the stent was removed without complications. Temporary tracheal stenting after PAS repair can be an effective therapeutic strategy in newborns with tracheal obstruction and allows timely weaning from ventilator support.
肺动脉吊带(PAS)是一种罕见疾病,常伴有严重的气管软化和狭窄。我们报告了一例 2 天的新生儿,因 PAS 接受了紧急手术,术后需要长时间的呼吸支持。术后 5 天,因气管软化和诊断性支气管镜检查后气管黏膜撕裂导致严重气道阻塞,在气管分叉以上行临时气道支架置入术。术后 2 天,患儿可拔管,2 周后无并发症取出支架。PAS 修复术后行临时气管支架置入可为存在气管梗阻的新生儿提供一种有效的治疗策略,可使患儿及时脱离呼吸机支持。