Tavusbay Cengiz, Genç Hüdai, Karaca İrfan, Atahan Kemal, Hacıyanlı Mehmet, Türk Erdal
Department of General Surgery, İzmir Katip Çelebi University Atatürk Training and Research Hospital, İzmir, Turkey.
Department of Pediatric Surgery, Medical Park İzmir Hospital, İzmir, Turkey.
Turk J Surg. 2017 Sep 1;33(3):205-208. doi: 10.5152/turkjsurg.2017.3193. eCollection 2017.
Anorectal malformations are rare occurrences characterized by the absence or abnormal localization of the anus. Clinical manifestations can vary from mild forms that require only minor surgery to more complicated cases that must be managed with multi-staged surgery. In this report, our aim is to present the clinical characteristics, management, and treatment outcome of an adult patient with an anorectal malformation with a vestibular fistula that was successfully repaired by posterior sagittal anorectoplasty (PSARP) and to discuss the case in the light of the relevant literature. We also would like to underline the fact that primary anorectal malformations can, although rarely, be observed in adult patients. A 26-year-old female patient presented with an imperforate anus and constipation with feces passing through a fistula located at the distal part of her vagina. She was continent for solid feces, but had leakage of flatus and fecal soiling. She also had concurrent left renal agenesis. A posterior sagittal anorectoplasty was successfully performed without a colostomy. The patient was discharged uneventfully on the postoperative 8th day. The patient was fully continent during a control visit after seven years of follow-up. Posterior sagittal anorectoplasty is a technique that can be successfully used in adult patients with anorectal malformations.
肛门直肠畸形是一种罕见的病症,其特征为肛门缺失或位置异常。临床表现从仅需小手术的轻症形式到必须通过多阶段手术治疗的更复杂病例不等。在本报告中,我们的目的是呈现一名患有前庭瘘的肛门直肠畸形成年患者的临床特征、治疗及治疗结果,该患者通过后矢状位肛门直肠成形术(PSARP)成功修复,并根据相关文献对该病例进行讨论。我们还想强调,原发性肛门直肠畸形虽然罕见,但在成年患者中也可观察到。一名26岁女性患者因肛门闭锁及便秘就诊,粪便经位于阴道远端的瘘管排出。她能控制固体粪便,但有气体泄漏和粪便污染。她还并发左肾缺如。成功进行了后矢状位肛门直肠成形术,未行结肠造口术。患者术后第8天顺利出院。经过7年随访,患者在复诊时完全能够控制排便。后矢状位肛门直肠成形术是一种可成功用于治疗成年肛门直肠畸形患者的技术。