Salomão Renan, Canêdo Nathalie Henriques Silva, Abrão Guilherme P, Lima Carlos, Acioly Marcus André
Division of Neurosurgery, Universidade Federal do Rio de Janeiro (UFRJ), Rio de Janeiro, RJ, Brazil.
Division of Neuropathology, UFRJ, Rio de Janeiro, Brazil.
Rev Assoc Med Bras (1992). 2017 Jul;63(7):564-565. doi: 10.1590/1806-9282.63.07.564.
Subacute necrotizing myelopathy (SNM) or Foix-Alajouanine syndrome is a rare disease characterized by progressive neurological dysfunction caused by a spinal dural arteriovenous fistula (AVF). Radiological diagnosis is usually suspected when there is intramedullary nonspecific enhancement and perimedullary flow voids. Ring-enhancement is rarely reported in the scope of AVF, which poses a diagnostic challenge and raises the suspicion of a spinal cord tumor. In such situations, biopsy can be required and delay proper diagnosis. We report the case of a patient with SNM, who underwent biopsy on the assumption of it being a spinal cord tumor.
亚急性坏死性脊髓病（SNM）或福-阿二氏综合征是一种罕见疾病，其特征为脊髓硬脊膜动静脉瘘（AVF）导致的进行性神经功能障碍。当出现髓内非特异性强化和髓周血流空洞时，通常会怀疑为放射学诊断。在AVF范围内很少报告有环形强化，这带来了诊断挑战，并引发了对脊髓肿瘤的怀疑。在这种情况下，可能需要进行活检，从而延误正确诊断。我们报告了一例亚急性坏死性脊髓病患者的病例，该患者因被误诊为脊髓肿瘤而接受了活检。
