Department of Neurosurgery, Medical University of South Carolina, Charleston, South Carolina, USA.
Department of Neurosurgery, Medical University of South Carolina, Charleston, South Carolina, USA.
World Neurosurg. 2024 May;185:1-2. doi: 10.1016/j.wneu.2024.01.152. Epub 2024 Feb 1.
Foix-Alajouanine syndrome is a rare cause of spinal dural arteriovenous fistula that can cause irreversible myelopathy and paraplegia if not treated promptly. The complex nature of this pathology often leads to missed or delayed diagnosis regardless of broad workups executed. We present a symptomatically classic Foix-Alajouanine 68-year-old patient with an accelerated progression reaching stages of severe myelopathy in less than a year. Even with endovascular intervention, our patient was unable to recover neurologically. Including appropriate spinal imaging early in the workup for Foix-Alajouanine syndrome is necessary to halt or treat this disease process.
福-艾-拉焦奥纳尼综合征是一种罕见的脊髓硬脑膜动静脉瘘的病因，如果不及时治疗，可能导致不可逆转的脊髓病和截瘫。尽管进行了广泛的检查，但由于这种病理学的复杂性，常常导致漏诊或延迟诊断。我们报告了一例症状典型的福-艾-拉焦奥纳尼 68 岁患者，其病情进展迅速，不到一年就达到严重脊髓病的阶段。即使进行了血管内介入治疗，我们的患者也无法在神经功能上恢复。在福-艾-拉焦奥纳尼综合征的检查中早期包括适当的脊柱成像，对于阻止或治疗这种疾病过程是必要的。
