Ogasawara Nobuhiko, Sato Kenichiro, Tsutsumiuchi Michiko, Kanzaki Mami, Uesaka Yoshikazu
Department of Neurology, Toranomon Hospital, Japan.
Okinaka Memorial Institute for Medical Research, Japan.
Intern Med. 2017 Dec 1;56(23):3179-3181. doi: 10.2169/internalmedicine.9185-17. Epub 2017 Oct 11.
A 70-year-old man with myotonic dystrophy (MD) showed repetitive vomiting and decreased food ingestion. These symptoms were caused by acute mass of steak impaction occluding the esophagus, known as "steakhouse syndrome," which may have occurred in response to esophageal functional changes following gastrointestinal involvement due to MD pathology. The occluding food was successfully removed endoscopically, and his symptoms resolved without relapse. Our case suggests that MD patients can present with "steakhouse syndrome" due to bolus food impaction occluding the esophagus as one of their gastrointestinal manifestations, which underscores the need for its consideration in MD patients presenting with similar symptoms.
一名患有强直性肌营养不良（MD）的70岁男性出现反复呕吐和食物摄入减少的症状。这些症状是由一块牛排急性嵌顿阻塞食管引起的，即所谓的“牛排馆综合征”，这可能是由于MD病理导致胃肠道受累后食管功能改变所致。阻塞的食物通过内镜成功取出，他的症状得以缓解且未复发。我们的病例表明，MD患者可能会因大块食物嵌顿阻塞食管而出现“牛排馆综合征”，这是其胃肠道表现之一，这突出了在出现类似症状的MD患者中考虑该综合征的必要性。
