Hayashi Masamichi, Imaizumi Kazuyoshi, Hattori Hidekazu, Toyama Hiroshi, Okazawa Mitsushi
Department of Internal Medicine, Division of Respiratory Medicine and Clinical Allergy Fujita Health University Toyoake Japan.
Department of Radiology Fujita Health University Toyoake Japan.
Respirol Case Rep. 2017 Oct 5;5(6):e00273. doi: 10.1002/rcr2.273. eCollection 2017 Nov.
We present a rare case of a branching anomaly of the aortic arch that resulted in wheezing and dyspnoea. The patient was a 60-year-old male with severe wheezing from babyhood, originally diagnosed with severe bronchial asthma. On auscultation, the inspiratory and expiratory wheezes appeared when the patient leaned forward. He also had difficulty in swallowing solid mass. Tests for airway reversibility and hyperresponsiveness were negative, and asthma treatment was ineffective. He had a right aortic arch. A barium oesophagogram and endoscopic examination indicated narrowing of the oesophagus from behind. Three-dimensional reconstruction of enhanced chest CT images indicated a right aortic arch and an aberrant enlarged left innominate artery, which compressed and narrowed the oesophagus and trachea from behind. Although the patient had been diagnosed with intractable bronchial asthma, his symptoms were more likely caused by this mechanical narrowing as wheezing and dyspnoea disappeared completely after total aortic arch replacement operation.
我们报告一例罕见的主动脉弓分支异常导致喘息和呼吸困难的病例。患者为一名60岁男性,自幼患有严重喘息,最初被诊断为重度支气管哮喘。听诊时,患者向前倾时出现吸气和呼气性喘息。他吞咽固体食物也有困难。气道可逆性和高反应性测试均为阴性,哮喘治疗无效。他有一个右位主动脉弓。钡餐食管造影和内镜检查显示食管后方狭窄。胸部增强CT图像的三维重建显示右位主动脉弓和一条异常增粗的左无名动脉,该动脉从后方压迫并使食管和气管变窄。尽管该患者曾被诊断为顽固性支气管哮喘,但他的症状更可能是由这种机械性狭窄引起的,因为在全主动脉弓置换手术后,喘息和呼吸困难完全消失了。