Ito Yuhei, Arita Machiko, Kumagai Shogo, Takei Reoto, Noyama Maki, Tokioka Fumiaki, Nagamoto Takumi, Kawakita Chieko, Asano Kenichiro, Okita Chika, Ishida Tadashi
Department of Respiratory Medicine, Kurashiki Central Hospital, Japan.
Department of Endocrinology and Rheumatology, Kurashiki Central Hospital, Japan.
Intern Med. 2018 Jan 1;57(1):81-84. doi: 10.2169/internalmedicine.8984-17. Epub 2017 Oct 16.
IgA vasculitis (IgAV) commonly occurs in young children, who present with a tetrad of purpura, abdominal pain, arthralgia and nephritis. Diffuse alveolar hemorrhage (DAH) is a rare complication of IgAV. We herein report an adult case of IgAV with a presentation of DAH and nephritis (pulmonary renal syndrome, PRS), but without other typical manifestations, such as purpura, abdominal pain and arthralgia. A 33-year-old man presented with hemoptysis and a low-grade fever and was diagnosed to have IgAV based on the results of a renal biopsy. Treatment with corticosteroids, cyclophosphamide, and plasmapheresis was effective. IgAV should therefore be considered in the differential diagnosis of adult PRS.
IgA 血管炎(IgAV)常见于幼儿,表现为紫癜、腹痛、关节痛和肾炎四联征。弥漫性肺泡出血(DAH)是 IgAV 的一种罕见并发症。我们在此报告一例成年 IgAV 病例,该患者表现为 DAH 和肾炎(肺肾综合征,PRS),但无紫癜、腹痛和关节痛等其他典型表现。一名 33 岁男性出现咯血和低热,根据肾活检结果诊断为 IgAV。使用糖皮质激素、环磷酰胺和血浆置换治疗有效。因此,在成人 PRS 的鉴别诊断中应考虑 IgAV。