Lucchi Chiara, Marchiò Maddalena, Caramaschi Elisa, Giordano Carmela, Giordano Rocco, Guerra Azzurra, Biagini Giuseppe
Laboratory of Experimental Epileptology, Department of Biomedical, Metabolic and Neural Sciences, University of Modena and Reggio Emilia, 41125 Modena, Italy.
Pediatric Neurology, Polyclinic Hospital, 41124 Modena, Italy.
Pharmaceuticals (Basel). 2017 Oct 20;10(4):82. doi: 10.3390/ph10040082.
The ketogenic diet (KD) is increasingly used to treat epilepsy refractory to antiepileptic drugs and other neurological disorders. In animal models, the KD was found to increase the threshold to seizures induced by different convulsive stimulations. However, in models in which suprathreshold stimuli were used, a paradoxical seizure worsening was consistently observed in KD-fed animals. To better define this phenomenon, we characterized the electrographic response to seizures induced in mice which were treated with the KD, and then corneally stimulated at 6-Hz in four different sessions. We also evaluated the electroencephalogram (EEG) in three patients in which the KD was associated with a paradoxical worsening of epileptic seizures. Although seizures were initially less severe, a remarkable prolongation of the electrographic response was observed in mice receiving the KD from the second session of 6-Hz corneal stimulation and onwards. The EEG was also markedly altered in the presence of progressive seizure aggravation observed in children treated with the KD, specifically one affected by Lennox-Gastaut syndrome and two by type I lissencephaly,. These results suggest that when seizures are induced or recur because of resistance to therapeutic interventions, the KD may change the EEG by potentiating the electrographic epileptic activity.
生酮饮食(KD)越来越多地用于治疗对抗癫痫药物难治的癫痫以及其他神经系统疾病。在动物模型中,发现生酮饮食可提高由不同惊厥刺激诱导的癫痫发作阈值。然而,在使用阈上刺激的模型中,始终观察到喂食生酮饮食的动物出现矛盾的癫痫发作恶化。为了更好地定义这一现象,我们对接受生酮饮食治疗的小鼠癫痫发作的电图反应进行了表征,然后在四个不同时段以6赫兹频率进行角膜刺激。我们还评估了三名患者的脑电图(EEG),在这些患者中,生酮饮食与癫痫发作的矛盾性恶化有关。尽管最初癫痫发作不太严重,但从第二次6赫兹角膜刺激开始,在接受生酮饮食的小鼠中观察到电图反应显著延长。在用生酮饮食治疗的儿童中,尤其是一名患有伦诺克斯 - 加斯东综合征和两名患有I型无脑回畸形的儿童,在癫痫发作逐渐加重的情况下,脑电图也有明显改变。这些结果表明,当癫痫发作由于对治疗干预的抵抗而诱发或复发时,生酮饮食可能通过增强电图癫痫活动来改变脑电图。