Maheswari S Uma, Sampath V, Ramesh A
Department of Dermatology, Madras Medical College and Rajiv Gandhi Government General Hospital, Chennai, Tamil Nadu, India.
Indian J Dermatol Venereol Leprol. 2018;84(2):169-173. doi: 10.4103/ijdvl.IJDVL_727_16.
Granulomatous slack skin syndrome is a rare variant of cutaneous T-cell lymphoma (mycosis fungoides). It is characterized clinically by redundant skin folds, which show a predilection towards flexural areas such as the axilla and the groin. Histologically, it shows a granulomatous T-cell infiltrate and loss of elastic tissue. It has an indolent but progressive course; and is usually refractory to treatment. We report a unique case of slack skin syndrome, sparing the classical sites with rapid and unusual involvement of non-intertriginous areas.
肉芽肿性皮肤松弛综合征是皮肤T细胞淋巴瘤（蕈样肉芽肿）的一种罕见变异型。其临床特征为皮肤褶皱过多，好发于腋窝和腹股沟等屈侧部位。组织学上，表现为肉芽肿性T细胞浸润和弹性组织缺失。它病程缓慢但呈进行性发展，通常对治疗耐药。我们报告了一例独特的皮肤松弛综合征病例，未累及经典部位，而非间擦疹部位迅速且异常受累。
