肉芽肿性皮肤松弛症

Granulomatous slack skin.

作者信息

Teixeira Marta, Alves Rosário, Lima Margarida, Canelhas Aurea, Rosário Conceição, Selores Manuela

机构信息

Dept of Dermatology, Hospital Geral de Santo António, Rua D. Manuel II, Edifício Ex-CICAP, 4099-001 Porto, Portugal.

出版信息

Eur J Dermatol. 2007 Sep-Oct;17(5):435-8. doi: 10.1684/ejd.2007.0243. Epub 2007 Aug 2.

DOI:10.1684/ejd.2007.0243

PMID:17673389

Abstract

Granulomatous slack skin is an extremely rare subtype of cutaneous T-cell lymphoma characterized by the slow development of folds of lax skin, especially in flexural areas and histologically characterized by a granulomatous infiltrate with clonal T cells. Notwithstanding its indolent behavior, treatment is often disappointing. We describe an additional case of this rare disorder in a 44-year-old male patient.

摘要

肉芽肿性皮肤松弛症是皮肤T细胞淋巴瘤一种极其罕见的亚型，其特征为松弛皮肤褶皱发展缓慢，尤其在屈侧部位，组织学特征为伴有克隆性T细胞的肉芽肿浸润。尽管其进展缓慢，但治疗效果往往令人失望。我们描述了一名44岁男性患者的这一罕见疾病的另一病例。