Tsukamoto Masanori, Yokoyama Takeshi
Department of Dental Anesthesiology, Kyushu University Hospital, Fukuoka, Japan.
Department of Dental Anesthesiology, Faculty of Dental Science, Kyushu University, Fukuoka, Japan.
J Dent Anesth Pain Med. 2017 Sep;17(3):215-217. doi: 10.17245/jdapm.2017.17.3.215. Epub 2017 Sep 25.
Branchio-oto-renal syndrome (BOR) is a rare autosomal dominant disorder. The features include branchial cysts, hearing loss, ear malformation, preauricular pits, retrognathia, congenital heart disease, and renal abnormalities. However, anesthetic management of these patients has seldom been reported. We report a case in which general anesthesia was performed for dental treatment in a patient with BOR. Airway management, renal function, and hemodynamic changes can be of critical concern during anesthetic management. A 13-year-old girl diagnosed with BOR had severe right hearing loss, right external ear malformation, renal abnormalities, and postoperative patent ductus arteriosus (PDA). Dental extraction under general anesthesia was scheduled for a supernumerary tooth. The procedure was completed with sufficient urine volume, adequate airway management, and stable hemodynamics.
鳃-耳-肾综合征（BOR）是一种罕见的常染色体显性疾病。其特征包括鳃裂囊肿、听力丧失、耳部畸形、耳前凹、小颌畸形、先天性心脏病和肾脏异常。然而，关于这些患者的麻醉管理鲜有报道。我们报告一例为患有BOR的患者进行牙科治疗时实施全身麻醉的病例。在麻醉管理过程中，气道管理、肾功能和血流动力学变化可能是至关重要的关注点。一名13岁被诊断为BOR的女孩有严重的右耳听力丧失、右耳外耳畸形、肾脏异常以及术后动脉导管未闭（PDA）。计划在全身麻醉下拔除一颗多生牙。手术在尿量充足、气道管理得当和血流动力学稳定的情况下完成。
