Nakamura Yoshitsugu, Nakajima Hideto, Hosokawa Takafumi, Yamane Kazushi, Ishida Shimon, Kimura Fumiharu
Division of Neurology, Department of Internal Medicine IV, Osaka Medical College, Japan.
Intern Med. 2018 Jan 15;57(2):269-271. doi: 10.2169/internalmedicine.9190-17. Epub 2017 Nov 1.
We herein report the case of a 53-year-old man with cerebellar ataxia with anti-glutamic acid decarboxylase antibody (GAD-Ab) who mimicked Miller Fisher syndrome (MFS). He developed ophthalmoplegia, diplopia, and gait ataxia for one week. The serum and cerebrospinal fluid GAD-Ab titers were greatly increased, and the GAD-Ab index suggesting intrathecal antibody synthesis was elevated, while GQ1b-Ab was negative. After steroid pulse therapy and following prednisolone, his symptoms dramatically improved over the course of 11 months with the simultaneous decline of GAD-Ab titers. This case indicates that cerebellar ataxia with GAD-Ab can present with acute neurological findings mimicking MFS, and that steroid therapy has an excellent therapeutic effect.
我们在此报告一例53岁患有抗谷氨酸脱羧酶抗体(GAD-Ab)相关性小脑共济失调的男性患者,其临床表现酷似米勒-费雪综合征(MFS)。他出现眼肌麻痹、复视和步态共济失调达一周时间。血清和脑脊液中GAD-Ab滴度大幅升高,提示鞘内抗体合成的GAD-Ab指数升高,而GQ1b-Ab为阴性。在接受类固醇冲击治疗及泼尼松龙治疗后,他的症状在11个月内显著改善,同时GAD-Ab滴度下降。该病例表明,GAD-Ab相关性小脑共济失调可表现出酷似MFS的急性神经学表现,且类固醇治疗具有极佳的治疗效果。