Majdoub I, Kallel S, Hsairi M, Snoussi M, Charfi M, Ben Halima A, Frikha A, Weli M, Safi F, Gargouri L, Ben Halima N, Mahfoudh A, Ghorbel A, Bahloul Z
Service de pédiatrie, urgence et réanimation pédiatriques, CHU Hédi Chaker, 3029 Sfax, Tunisie.
Service d'oto-rhino-larynologie, CHU Habib Bourguiba, route El Ain km 0.5, Sfax, Tunisie.
Arch Pediatr. 2017 Dec;24(12):1249-1252. doi: 10.1016/j.arcped.2017.09.009. Epub 2017 Nov 20.
Sjögren syndrome is uncommon in children and occurs most often in association with autoimmune diseases (secondary Sjögren syndrome). We describe the clinical and biological features of a 7-year-old girl with primary Sjögren syndrome revealed by recurrent parotiditis.
A 7-year-old girl was referred for investigation of multiple episodes of parotid swelling since age 4 years, without systemic symptoms. The examination was unremarkable except for enlarged and painless parotid glands. Laboratory investigations and labial salivary gland biopsy revealed Sjögren syndrome without associated disease. Hydroxychloroquine was prescribed with clinical improvement.
Recurrent parotiditis in children is an uncommon condition. The onset of parotid swelling at 5 years or over deserves screening for disimmune disorders, sarcoidosis, or Sjögren syndrome. Diagnosis of Sjögren syndrome is based on diagnostic criteria.
干燥综合征在儿童中并不常见，最常与自身免疫性疾病相关（继发性干燥综合征）。我们描述了一名7岁原发性干燥综合征女童的临床和生物学特征，该患儿因复发性腮腺炎而被确诊。
一名7岁女童因自4岁起多次出现腮腺肿大前来就诊，无全身症状。除腮腺肿大且无痛外，体格检查无异常。实验室检查和唇腺活检显示为无相关疾病的干燥综合征。给予羟氯喹治疗后临床症状改善。
儿童复发性腮腺炎并不常见。5岁及以上出现腮腺肿大应筛查免疫性疾病、结节病或干燥综合征。干燥综合征的诊断基于诊断标准。
