Demircioglu F F, Böke E, Demircin M, Dagsali S, Küçükali T
Department of Cardiology, Gazi University School of Medicine, Ankara, Turkey.
Angiology. 1989 Mar;40(3):227-32. doi: 10.1177/000331978904000311.
Behçet's syndrome, a multisystem disorder, is characterized by recurrent oral and genital aphthous ulcerations, eye lesions, and skin changes. Other manifestations, although rare, may affect the nervous, gastrointestinal, or locomotor system, as well as veins and arteries. Vascular lesions occur in approximately 30% of reported cases. Although thrombosis in the larger veins is frequent, arterial thrombosis is somewhat less likely to occur. Only a few cases of arterial aneurysm have been documented in the literature. This report describes a patient who had suffered from Behçet's syndrome for fifteen years and in whom a complete obstruction of the inferior vena cava was demonstrated. An aortoiliac bypass was performed successfully, and the patient had had a good clinical recovery at long-term follow-up.
白塞病是一种多系统疾病,其特征为复发性口腔和生殖器阿弗他溃疡、眼部病变及皮肤改变。其他表现虽罕见,但可累及神经、胃肠或运动系统以及动静脉。约30%的报告病例出现血管病变。尽管大静脉血栓形成常见,但动脉血栓形成的可能性稍小。文献中仅记载了少数几例动脉动脉瘤病例。本报告描述了一名患有白塞病15年的患者,该患者下腔静脉完全阻塞。成功实施了主-髂动脉搭桥术,患者在长期随访中临床恢复良好。