Department of Dermatology, University of North Carolina at Chapel Hill, Chapel Hill, North Carolina, USA; School of Life Science and Biotechnology, Dalian University of Technology, Dalian, Liaoning, People's Republic of China.
Department of Dermatology, University of North Carolina at Chapel Hill, Chapel Hill, North Carolina, USA.
J Invest Dermatol. 2018 May;138(5):1032-1043. doi: 10.1016/j.jid.2017.11.031. Epub 2017 Dec 12.
Eosinophils are typically associated with unique inflammatory settings, including allergic inflammation and helminth infections. However, new information suggests that eosinophils contribute more broadly to inflammatory responses and participate in local immune regulation and the tissue remodeling/repair events linked with a variety of diseases. Eosinophilic infiltration has long been a histologic hallmark of bullous pemphigoid (BP), a subepidermal autoimmune blistering disease characterized by autoantibodies directed against basement membrane protein BP180. However, the exact role of eosinophils in disease pathogenesis remains largely unknown. We show here that eosinophils are necessary for IgE autoantibody-mediated BP blister formation in a humanized IgE receptor mouse model of BP. Disease severity is IgE dose dependent and correlates with the degree of eosinophil infiltration in the skin. Furthermore, IgE autoantibodies fail to induce BP in eosinophil-deficient mice, confirming that eosinophils are required for IgE-mediated tissue injury. Thus, eosinophils provide the cellular link between IgE autoantibodies and skin blistering in this murine model of BP. These findings suggest a role for eosinophils in autoimmune disease and have important implications for the treatment of BP and other antibody-mediated inflammatory and autoimmune diseases.
嗜酸性粒细胞通常与独特的炎症环境相关,包括过敏炎症和寄生虫感染。然而,新的信息表明,嗜酸性粒细胞更广泛地参与炎症反应,并参与局部免疫调节以及与多种疾病相关的组织重塑/修复事件。嗜酸性粒细胞浸润长期以来一直是大疱性类天疱疮 (BP) 的组织学特征,BP 是一种表皮下自身免疫性水疱病,其特征是针对基底膜蛋白 BP180 的自身抗体。然而,嗜酸性粒细胞在疾病发病机制中的确切作用在很大程度上仍然未知。我们在这里显示,嗜酸性粒细胞是 IgE 自身抗体介导的 BP 水疱形成所必需的,这是一种 BP 的人源化 IgE 受体小鼠模型。疾病严重程度与 IgE 剂量有关,并与皮肤中嗜酸性粒细胞浸润的程度相关。此外,IgE 自身抗体不能诱导嗜酸性粒细胞缺陷小鼠发生 BP,这证实了嗜酸性粒细胞是 IgE 介导的组织损伤所必需的。因此,嗜酸性粒细胞在该 BP 小鼠模型中提供了 IgE 自身抗体和皮肤水疱之间的细胞联系。这些发现表明嗜酸性粒细胞在自身免疫性疾病中具有作用,并对 BP 和其他抗体介导的炎症和自身免疫性疾病的治疗具有重要意义。