Shahcheraghi Gholam Hossain, Javid Mahzad
Department of Orthopaedic Surgery, Bone and Joint Diseases Research Center, Shiraz University of Medical Sciences, Shiraz, Iran.
JBJS Case Connect. 2017 Jul-Sep;7(3):e67. doi: 10.2106/JBJS.CC.16.00277.
Trevor disease (dysplasia epiphysealis hemimelica [DEH]) is a rare, intra-articular anomaly of cartilaginous overgrowth of the epiphysis. The usual presentation is on 1 side of the body and on 1 side of the epiphysis. The natural history of this disease is not clear because the lesions often are treated during childhood. Additionally, hip involvement is relatively uncommon; to our knowledge, total hip arthroplasty in a patient with DEH has not been reported previously. Our patient presented with previously untreated DEH of the hip joint, which had developed into a very unusual shape. He was treated with a total hip arthroplasty and had satisfactory functioning 2.5 years postsurgery.
Untreated DEH of the hip can lead to a very misshapen hip with a deformed femoral head and loss of the shape of the acetabulum, as well as stiffness due to an unusual shape and osteoarthritic changes. A total hip arthroplasty can give satisfactory functional results.
特雷弗病(半侧骨骺发育异常[DEH])是一种罕见的关节内骨骺软骨过度生长异常。通常表现为身体一侧和骨骺一侧受累。由于病变常在儿童期接受治疗,该疾病的自然病程尚不清楚。此外,髋关节受累相对少见;据我们所知,此前尚未报道过DEH患者行全髋关节置换术的情况。我们的患者表现为未经治疗的髋关节DEH,已发展成非常异常的形状。他接受了全髋关节置换术,术后2.5年功能良好。
未经治疗的髋关节DEH可导致髋关节严重畸形,股骨头变形,髋臼形态丧失,以及因异常形状和骨关节炎改变而导致的僵硬。全髋关节置换术可取得满意的功能效果。