Grafton Specialists, Auckland, New Zealand; and.
Eye Doctors, Ascot Hospital, Auckland, New Zealand.
Retin Cases Brief Rep. 2020 Fall;14(4):334-338. doi: 10.1097/ICB.0000000000000692.
Idiopathic retinal vasculitis, aneurysms, and neuroretinitis syndrome is a very rare primary retinal vasculitis. It seems to evolve in stages, where there is initially a florid vasculitis associated with aneurysm formation. Neuroretinitis and macula edema are common features. Subsequently, retinal ischemia ensues, leading to neovascularization. If untreated, further sight-threatening complications occur, including traction retinal detachment and secondary glaucoma.
Here, we describe a patient with early idiopathic retinal vasculitis, aneurysms, and neuroretinitis syndrome, who was treated with a combination of systemic immunosuppression and localized photocoagulation. There was substantial regression of the aneurysms and improvement of the macular edema. Treatment of the disorder should be based on the clinical stage and complications of the disorder.
As shown here, a multidisciplinary approach can be very helpful in managing patients with this severe sight-threatening disorder.
特发性视网膜血管炎、动脉瘤和神经视网膜炎综合征是一种非常罕见的原发性视网膜血管炎。它似乎分阶段演变，最初是伴有动脉瘤形成的明显血管炎。神经视网膜炎和黄斑水肿是常见特征。随后，视网膜缺血随之发生，导致新生血管形成。如果未经治疗，会出现进一步威胁视力的并发症，包括牵引性视网膜脱离和继发性青光眼。
在这里，我们描述了一名患有早期特发性视网膜血管炎、动脉瘤和神经视网膜炎综合征的患者，该患者接受了全身免疫抑制和局部光凝联合治疗。动脉瘤明显消退，黄斑水肿改善。这种疾病的治疗应基于疾病的临床阶段和并发症。
正如这里所展示的，多学科方法对于治疗这种严重威胁视力的疾病非常有帮助。
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