Hajji Meriam, Jebali Hela, Mzoughi Khadija, Zairi Ihssen, Kheder Rania, Fatma Lilia Ben, Rais Lamia, Kadouri Rokaya, Kraiem Sinda, Smaoui Wided, Krid Madiha, Beji Soumaya, Zouaghi Karim
Department of Nephrology, Dialysis and Transplantation, La Rabta Hospital, Tunis, Tunisia.
Department of Cardiology, Habib Thameur Hospital, Tunis, Tunisia.
Saudi J Kidney Dis Transpl. 2017 Nov-Dec;28(6):1443-1446. doi: 10.4103/1319-2442.220844.
Autosomal-dominant polycystic kidney disease (ADPKD) is a systemic disorder associated with various extrarenal complications. There is little information regarding the occurrence and distribution of cardiovascular abnormalities during the course of ADPKD. The major cardiovascular complications of ADPKD include valvulopathies and vascular ectasia. Aneurysm of the atrial septum (ASA) is a very rare manifestation in ADPKD. A 37-year-old woman who was diagnosed with ADPKD was admitted to our hospital for advanced renal failure. Pelvic computed tomography revealed multiple variable-sized cysts in both kidneys. Trans-thoracic echocardiography showed ASA while the patient was completely asymptomatic.
常染色体显性多囊肾病（ADPKD）是一种与多种肾外并发症相关的全身性疾病。关于ADPKD病程中心血管异常的发生和分布情况，相关信息较少。ADPKD的主要心血管并发症包括瓣膜病和血管扩张。房间隔动脉瘤（ASA）在ADPKD中是一种非常罕见的表现。一名37岁被诊断为ADPKD的女性因晚期肾衰竭入住我院。盆腔计算机断层扫描显示双肾有多个大小不一的囊肿。经胸超声心动图显示该患者存在ASA，但完全没有症状。
