Ekin Meryem Altin, Ugurlu Seyda Karadeniz, Cakalagaoglu Fulya
Department of Ophthalmology, Izmir Katip Celebi University, Ataturk Training and Research Hospital, Izmir, Turkey.
Department of Pathology, Izmir Katip Celebi University, Ataturk Training and Research Hospital, Izmir, Turkey.
Indian J Ophthalmol. 2018 Jan;66(1):160-163. doi: 10.4103/ijo.IJO_755_16.
Giant cell angiofibroma (GCA) is a recently reported rare soft-tissue tumor that can develop in various sites including orbit. Orbital GCAs were mainly located in the eyelid or extraconal regions such as lacrimal gland and conjunctiva. We report an atypical case of a GCA arising in the intraconal area of the orbit in a 65-year-old male patient. The tumor was excised in total by lateral orbitotomy. Histological and immunohistochemical features were consistent with the diagnosis of GCA. No recurrence was observed during the follow-up of over 2 years. GCA is a rare tumor that should be considered in the differential diagnosis of intraconal orbital tumors. Complete surgical removal is the current optimal treatment option.
巨细胞血管纤维瘤（GCA）是一种最近报道的罕见软组织肿瘤，可发生于包括眼眶在内的各种部位。眼眶GCA主要位于眼睑或眶锥外区域，如泪腺和结膜。我们报告一例非典型的GCA病例，发生于一名65岁男性患者眼眶的眶锥内区域。通过外侧眶切开术将肿瘤完整切除。组织学和免疫组化特征与GCA的诊断相符。在超过2年的随访期间未观察到复发。GCA是一种罕见肿瘤，在眶锥内眼眶肿瘤的鉴别诊断中应予以考虑。完整手术切除是目前最佳的治疗选择。
