Gomez-Larrauri Ana, Galloway Simon, Niven Rob
MAHSC, The University of Manchester and University Hospital of South Manchester, Southmoor Road, M23 9LT, Manchester, UK.
Respiratory Department, University Hospital of Araba, Jose Atxotegi, s/n, 01009, Vitoria-Gasteiz, Araba, Spain.
Respir Med Case Rep. 2017 Dec 18;23:80-82. doi: 10.1016/j.rmcr.2017.12.008. eCollection 2018.
Achalasia is an uncommon oesophageal motor disorder characterized by failure of relaxation of the lower oesophageal sphincter and muscle hypertrophy, resulting in a loss of peristalsis and a dilated oesophagus. Gastrointestinal symptoms are invariably present in all cases of achalasia observed in adults. We report a case of a 34 year-old female patient with long standing history of asthma-like symptoms, labelled as uncontrolled and steroid resistant asthma with no gastrointestinal manifestations. Thoracic CT scan revealed a massive oesophagus due to achalasia, which caused severe tracheomalacia as a result of tracheal compression. Her symptoms regressed completely after a laparoscopic Heller myotomy surgery intervention.
贲门失弛缓症是一种罕见的食管运动障碍，其特征为食管下括约肌松弛失败和肌肉肥大，导致蠕动丧失和食管扩张。在所有成人贲门失弛缓症病例中，胃肠道症状始终存在。我们报告一例34岁女性患者，有长期类似哮喘症状的病史，被诊断为未控制的类固醇抵抗性哮喘，无胃肠道表现。胸部CT扫描显示因贲门失弛缓症导致食管巨大，进而因气管受压引起严重气管软化。在腹腔镜下Heller肌切开术干预后，她的症状完全消退。
