Shah Abhidha, Kaswa Amol, Jain Sonal, Goel Atul
Department of Neurosurgery, K.E.M. Hospital and Seth G.S. Medical College, Parel, Mumbai, Maharashtra, India.
Neurol India. 2018 Jan-Feb;66(1):147-150. doi: 10.4103/0028-3886.222853.
We report a series of four patients aged 4, 5, 14, and 27 years (1 male and 3 female patients) with severe shortening of the neck and torticollis since early childhood who presented with complaint of pain in the nape of neck as the primary symptom. All four patients had relatively well preserved neurological functions. One patient had vertical mobile and reducible atlantoaxial dislocation, and 3 patients had anteroposterior mobile and reducible dislocation. There was assimilation of atlas in 1 patient. The arch of atlas was bifid in 3 patients. Two patients underwent atlantoaxial fixation. Both the patients were relieved of neck pain after their surgery. The potential surgical difficulties due to the presence of severe shortening of neck height and marginal presenting symptoms favored conservative observation in the other 2 patients. Follow-up ranged from 6 to 84 months. All patients are functionally and socially active.
我们报告了一系列4名患者，年龄分别为4岁、5岁、14岁和27岁（1名男性患者和3名女性患者），自幼儿期起就有严重的颈部缩短和斜颈，以颈部疼痛为主要症状就诊。所有4名患者的神经功能相对保存良好。1例患者有垂直活动且可复位的寰枢椎脱位，3例患者有前后活动且可复位的脱位。1例患者有寰椎融合。3例患者的寰椎弓为双裂。2例患者接受了寰枢椎固定术。两名患者术后颈部疼痛均缓解。由于颈部高度严重缩短和边缘性症状的存在，另外2例患者存在潜在的手术困难，因此倾向于保守观察。随访时间为6至84个月。所有患者在功能和社交方面均活跃。
