Johnson Erik R, Korchak Michael E, Goodglick Todd A, Johal Jasbir S, Dufresne Craig R, Sabet Sina J
Department of Ophthalmology, MedStar Georgetown University Hospital, Washington, DC.
Department of Ophthalmology, MedStar Washington Hospital Center, Washington, DC.
Ocul Oncol Pathol. 2017 Dec;4(1):57-60. doi: 10.1159/000477734. Epub 2017 Jul 26.
Pigmented epithelioid melanocytoma (PEM) of the skin has been rarely reported in ophthalmology. The purpose of this case report is to present a young male born with a progressive, hyperpigmented lesion involving the orbit and intracranial cavity diagnosed as PEM. The case is unique given the young age and the size, multifocality, and growth of this tumor. Identification of this lesion is paramount due to its low-grade malignant potential.
皮肤色素性上皮样黑素细胞瘤（PEM）在眼科领域鲜有报道。本病例报告旨在呈现一名患有累及眼眶和颅内腔的进行性色素沉着病变的年轻男性，该病变被诊断为PEM。鉴于该肿瘤的患者年轻、体积大、具有多灶性且不断生长，此病例较为独特。鉴于其低级别恶性潜能，识别该病变至关重要。
