烟雾病综合征患儿椎动脉起源和走行的多种异常及迷走右锁骨下动脉
Multiple anomalies in the origin and course of vertebral arteries and aberrant right subclavian artery in a child with moyamoya syndrome.
作者信息
Beyaz Pınar, Khan Nadia, Baltsavias Gerasimos
机构信息
UniversitatsSpital Zurich Klinik fur Neuroradiologie, Zurich, Switzerland.
Moyamoya Center, Universitats-Kinderspital Zurich, Zurich, Switzerland.
出版信息
BMJ Case Rep. 2018 Jan 23;2018:bcr-2017-013464. doi: 10.1136/bcr-2017-013464.
Here we report, for the first time, a combination of five-vessel aortic arch, anomalous origin of the right vertebral artery (VA) from the common carotid artery (CCA), an aberrant right subclavian artery (SCA), and bilateral symmetrical segmental agenesis of VAs.In this case report, we present a patient with moyamoya syndrome (MMS) and Down syndrome (DS) who has bilateral symmetrical segmental agenesis of VAs, left VA originating from aortic arch and anomalous origin of right VA arising from CCA in combination with an aberrant right SCA. Therefore, five vessels are originating from aortic arch. Here, we report, for the first time, a combination of five-vessel aortic arch with an aberrant right SCA and symmetrical segmental agenesis of both VAs. The possible embryological mechanisms of the anomalies as well as an relation with MMS and DS are discussed.
在此，我们首次报告了一种五支血管主动脉弓、右椎动脉（VA）起源于颈总动脉（CCA）异常、右锁骨下动脉（SCA）异常以及双侧椎动脉节段性缺如的组合情况。在本病例报告中，我们呈现了一名患有烟雾病综合征（MMS）和唐氏综合征（DS）的患者，其双侧椎动脉节段性缺如，左椎动脉起源于主动脉弓，右椎动脉起源于CCA异常，同时伴有右SCA异常。因此，有五支血管起源于主动脉弓。在此，我们首次报告了五支血管主动脉弓与右SCA异常以及双侧椎动脉节段性缺如的组合情况。讨论了这些异常可能的胚胎学机制以及与MMS和DS的关系。
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