Yang Min-Xia, Zhao Zhen-Hua, Yang Jian-Feng, Chen Bing, Shen Xun-Ze, Wei Jian-Guo, Wang Bo-Yin
Department of Radiology Department of Pathology, Shaoxing People's Hospital, Shaoxing Hospital of Zhejiang University, Shaoxing, Zhejiang Province, China.
Medicine (Baltimore). 2017 Dec;96(52):e8967. doi: 10.1097/MD.0000000000008967.
Plexiform fibromyxoma (PF) is an extremely rare mesenchymal tumor of the stomach, and its radiological findings have not been well described. Here, we analyzed the imaging features of a case of PF. To our knowledge, this is a rare reported case with a remarkable cystic change in the imaging literature.
A previously healthy 50-year-old woman presented with a 1-day history of abdominal pain. Then, she underwent computed tomography (CT) and magnetic resonance imaging (MRI). A cystic-solid well-circumscribed extraluminal mass was located in the posterior wall of the gastric upper body. The solid portion appeared as heterogeneous attenuation/intensity with progressive enhancement while the cystic region had no enhancement.
The potential for malignancy could not be excluded.
Laparoscopic partial gastric resection was performed.
Based on pathological findings, a diagnosis of PF was made. The patient was alive without any recurrence or metastasis of the tumor after 2 years of follow-up.
As far as we know, a gastric PF with a remarkable cystic change has never been reported. Additionally, the tumor exhibited a progressive enhancement pattern which is a characteristic radiographic feature in our case. Our report may help increase the awareness of this rare but important new disease entity.
丛状纤维黏液瘤（PF）是一种极其罕见的胃间叶性肿瘤，其影像学表现尚未得到充分描述。在此，我们分析了1例PF的影像学特征。据我们所知，这是影像学文献中罕见的1例有显著囊性改变的报道病例。
一名既往健康的50岁女性，有1天的腹痛病史。随后，她接受了计算机断层扫描（CT）和磁共振成像（MRI）检查。胃体上部后壁有一个边界清晰的囊实性腔外肿块。实性部分表现为不均匀的衰减/信号强度，呈渐进性强化，而囊性区域无强化。
不能排除恶性可能。
行腹腔镜胃部分切除术。
根据病理结果，诊断为PF。随访2年，患者存活，肿瘤无复发或转移。
据我们所知，从未有过伴有显著囊性改变的胃PF的报道。此外，该肿瘤表现出渐进性强化模式，这是我们病例中的一个特征性影像学表现。我们的报告可能有助于提高对这种罕见但重要的新疾病实体的认识。
