Akyel Nazlı Gülsüm, Alımlı Ayşe Gül, Demirkan Tülin Hakan, Sivri Mesut
Department of Radiology, Ankara Child Health and Diseases Hematology Oncology Training and Research Hospital, University of Health Sciences, Şehit Ömer Halisdemir Cad. Kurtdereli Sok, 06110, Ankara, Altındağ, Turkey.
Childs Nerv Syst. 2018 Jul;34(7):1407-1410. doi: 10.1007/s00381-018-3747-4. Epub 2018 Feb 14.
Persistent craniopharyngeal canal (PCC) is a rare anomaly of the base of the skull. PCC is defined as a well-corticated osseous canal, extending from the roof of the nasopharynx to the base of the sella over the course of the sphenoid corpus. We reported a PCC case with unique associations. The magnetic resonance imaging findings are discussed.
We report a case of a 2-year-old boy with persistent craniopharyngeal canal, bilateral microphtalmia with large colobomatous cyst, and ectopic adenohypophysis with Rathke cleft cyst. He also has ectopic neurohypophysis and optic atrophy.
The presence of orbital and optic tract malformations, craniofacial and intracranial anomalies, and tumors can accompany craniopharyngeal canals (CCs). MRI is helpful in the evaluation of PCC and associated anomalies in these patients.
持续性颅咽管（PCC）是一种罕见的颅底异常。PCC被定义为一条皮质良好的骨性管道，从鼻咽顶部延伸至蝶骨体部上方的鞍底。我们报告了一例具有独特关联的PCC病例，并讨论了磁共振成像结果。
我们报告了一例2岁男孩，患有持续性颅咽管、双侧小眼畸形伴巨大裂孔囊肿、异位腺垂体伴拉克囊肿。他还患有异位神经垂体和视神经萎缩。
眼眶和视束畸形、颅面及颅内异常和肿瘤可与颅咽管（CCs）并存。MRI有助于评估这些患者的PCC及相关异常。
