Department of Family Medicine University of Pittsburgh School of Medicine, Altoona, USA.
Department of Radiology Penn State Hershey Medical Center, Hershey, USA.
J Radiol Case Rep. 2023 Oct 31;17(10):14-20. doi: 10.3941/jrcr.v17i8.4707. eCollection 2023 Oct.
Persistent craniopharyngeal canal (PCC) is a rare congenital anomaly that appears as a linear well-corticated canal running from the sella through the clivus and into the nasopharynx. Case reports of this anomaly have shown it is associated with a range of craniofacial defects, pituitary abnormalities, and meningoencephaloceles. It predisposes patients to bacterial meningitis. In this case a 46-year-old gentleman presenting for preoperative planning for surgical drainage of Potts Puffy tumor was found to have a PCC on CT and MRI. Imaging also demonstrated the presence of chronic inflammation and a fistula extending from the tract into the sphenoid sinus. This unusual presentation of a PCC with a sphenoid sinus fistula broadens the potential clinical presentations of PCC and further emphasizes the ability of this anomaly to serve as a conduit for CNS infection.
持续颅咽管(PCC)是一种罕见的先天性异常,表现为从鞍区穿过斜坡延伸至鼻咽部的线性、皮质良好的管道。该异常的病例报告显示,其与一系列颅面缺陷、垂体异常和脑膜脑膨出有关。它使患者易患细菌性脑膜炎。在本例中,一位 46 岁的男性因术前计划行手术引流波特氏隆起而就诊,在 CT 和 MRI 上发现存在 PCC。影像学还显示存在慢性炎症和从管道延伸至蝶窦的瘘管。这种具有蝶窦瘘管的不常见 PCC 表现拓宽了 PCC 的潜在临床表现,并进一步强调了该异常作为中枢神经系统感染的通道的能力。