特发性肺纤维化：执业护士指南

Vega-Olivo Michelle, Criner Gerard J

Michelle Vega-Olivo is a CRNP, FNP-BC at Temple University, Philadelphia, Pa. Gerard J. Criner is a professor and chair at the Department of Thoracic Medicine and Surgery at Temple University, School of Medicine, Philadelphia, Pa.

Nurse Pract. 2018 May 17;43(5):48-54. doi: 10.1097/01.NPR.0000531121.07294.36.

Idiopathic pulmonary fibrosis (IPF) is a rare disease characterized by decline in lung function, dyspnea, and cough. The clinical course of IPF is variable and unpredictable. Early referral to specialists is key to ensure timely and accurate diagnosis. Two antifibrotic drugs (nintedanib and pirfenidone) have been approved for the treatment of IPF.

特发性肺纤维化（IPF）是一种罕见疾病，其特征为肺功能下降、呼吸困难和咳嗽。IPF的临床病程多变且不可预测。尽早转诊至专科医生处是确保及时准确诊断的关键。两种抗纤维化药物（尼达尼布和吡非尼酮）已被批准用于治疗IPF。